Abstract:

We analyzed literature data and demonstrate own clinical case of stillborn with prune belly syndrome. Development of prune belly syndrome is a rare but severe pathology of the fetus. We have indicated the frequency, causes of development and also clinical and morphological features of this anomaly, including in combination with the cloaca. Noted that such families need genetic testing due to the high of redevelopment of similar anomalies. We showed possibilities of postmortem computed tomography in identifying concomitant pathology, including three dimensional reconstruction of bone tissue. It was concluded that carrying out postmortem CT as complement to the autopsy is expedient.

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